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| CASE REPORT |
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| Year : 2020 |
Volume
: 30 | Issue : 2 | Page
: 240-243 |
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Fallot type of absent pulmonary valve syndrome - A case report
Divya B Desai, Neeti P Mathur, Arnab Marik
Department of Radiodiagnosis, D Y Patil Hospital and Research Center, Sector-5, Nerul, Navi Mumbai, Maharashtra, India
Correspondence Address:
Dr. Divya B Desai
204, Siddharth Apartment, Behind Kakdia Complex, Ghod Dod Road, Surat - 395 007, Gujarat
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/ijri.IJRI_508_19
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Absent pulmonary valve syndrome (APVS) is a rare congenital cardiac malformation characterized by absent, dysplastic, or rudimentary pulmonary valve leaflets in association with other cardiac anomalies. It has an incidence of 3-6% in cases of tetralogy of Fallot (TOF) and 0.2-0.4% of live-born infants with congenital heart disease (CHD). Absent pulmonary valve leads to dilated main pulmonary artery; presenting as a pulsatile, paracardiac cystic lesion on antenatal ultrasound (USG). We report a case of this rare anomaly in association with ventricular septal defect (VSD), TOF, and left axis deviation of heart detected at 23 weeks of gestation.
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