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Year : 2006  |  Volume : 16  |  Issue : 4  |  Page : 653-654
Congenital orbital cyst with micro-ophthalmos

Department of Radiodiagnosis, Gandhi Medical College and Hamidia Hospital, Bhopal, India

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Date of Submission25-Sep-2005
Date of Acceptance10-Jun-2006

Keywords: Coloboma, micro-ophthalmos, orbital cyst

How to cite this article:
Malik R, Pandya V K, Pawasthi. Congenital orbital cyst with micro-ophthalmos. Indian J Radiol Imaging 2006;16:653-4

How to cite this URL:
Malik R, Pandya V K, Pawasthi. Congenital orbital cyst with micro-ophthalmos. Indian J Radiol Imaging [serial online] 2006 [cited 2020 Dec 5];16:653-4. Available from:

   Introduction Top

Cystic lesions of the orbit are frequently encountered in the radiological assessment of orbital pathologies. Knowledge of these cystic lesions & their imaging appearance enables radiologist to make the correct diagnosis. The orbital cysts can be developmental or acquired. The colobomatous cysts are very rare developmental lesions [1].

A coloboma is a congenital or acquired notch, gap or fissure in which a portion of normal tissue is absent. Any part of the eye may be affected, however, typically the cleft appears in the inferonasal quadrant of the globe [2]. The optic nerve head is also commonly involved resulting in central excavation of the disc. More than 60% of cases are bilateral [3]. A coloboma may be an isolated finding or a part of a complex syndrome [3],[4].

Here we report a case of microphthalmos with congenital orbital cyst (Colobomatous cyst).

   Material & Method Top

A 20 years male patient presented with unilateral increasing proptosis of right eye with loss of vision in the right eye since birth & was referred to the department of Radiodiagnosis for CT scan of the orbits.

CT (axial & coronal) showed a somewhat oval lesion of attenuation < +30HU in its major part, involving the lateral part of right orbit. The right eye was very small with a small ramnant of eye lens [Figure - 1],[Figure - 2]. The cyst was displacing & stretching the optic nerve medially. The axial length of left eye was also reduced measuring 20mm.

On B-scan the lesion was shown to be entirely cystic occupying majority of the right orbit & communicating with a small eye ball (microophthalmos).

   Discussion Top

The microphtalmies can be of three types(5):

simple microphtalmy with partially preserved vision;

microphtalmy associated with other noncolobomatus anomalies; microphtalmiecolobomateuse with or without orbital cyst where there is small eye ball associated with a colobomatous cyst.

The size of cyst is usually larger than the eye ball.

On imaging, cleft in the globe may be visualized however, the tunnel-like connection between the eye and the cyst is often very thin and difficult to image[1]. CT can demonstrate the anatomic relationship of the cyst to the globe.

   References Top

1.S Vashisht, S Ghai, P Hatimota, S Ghai, SM Betharia Ind J Radiol Imag 2003 13:2:139-144  Back to cited text no. 1    
2.Kaufman LM, Villablanca JP, Mafee MF. Diagnostic imaging of cystic lesions in the child's orbit. Radiol Clinics of North America 1998; 36: 1149- 1163.  Back to cited text no. 2    
3.Kindler P. Morning glory syndrome: unusual congenital optic disc anomaly. Am J Ophthalmol 1970; 69: 376- 384.  Back to cited text no. 3  [PUBMED]  
4.Pagon RA. Ocular coloboma. Surv Ophthalmol 1981; 25: 223- 236.  Back to cited text no. 4  [PUBMED]  [FULLTEXT]

Correspondence Address:
R Malik
Department of Radiodiagnosis, Gandhi Medical College and Hamidia Hospital, Bhopal
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Source of Support: None, Conflict of Interest: None

DOI: 10.4103/0971-3026.32292

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  [Figure - 1], [Figure - 2]

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