Indian Journal of Radiology and Imaging Indian Journal of Radiology and Imaging

CASE REPORT
Year
: 2020  |  Volume : 30  |  Issue : 2  |  Page : 240--243

Fallot type of absent pulmonary valve syndrome - A case report


Divya B Desai, Neeti P Mathur, Arnab Marik 
 Department of Radiodiagnosis, D Y Patil Hospital and Research Center, Sector-5, Nerul, Navi Mumbai, Maharashtra, India

Correspondence Address:
Dr. Divya B Desai
204, Siddharth Apartment, Behind Kakdia Complex, Ghod Dod Road, Surat - 395 007, Gujarat
India

Absent pulmonary valve syndrome (APVS) is a rare congenital cardiac malformation characterized by absent, dysplastic, or rudimentary pulmonary valve leaflets in association with other cardiac anomalies. It has an incidence of 3-6% in cases of tetralogy of Fallot (TOF) and 0.2-0.4% of live-born infants with congenital heart disease (CHD). Absent pulmonary valve leads to dilated main pulmonary artery; presenting as a pulsatile, paracardiac cystic lesion on antenatal ultrasound (USG). We report a case of this rare anomaly in association with ventricular septal defect (VSD), TOF, and left axis deviation of heart detected at 23 weeks of gestation.


How to cite this article:
Desai DB, Mathur NP, Marik A. Fallot type of absent pulmonary valve syndrome - A case report.Indian J Radiol Imaging 2020;30:240-243


How to cite this URL:
Desai DB, Mathur NP, Marik A. Fallot type of absent pulmonary valve syndrome - A case report. Indian J Radiol Imaging [serial online] 2020 [cited 2020 Sep 18 ];30:240-243
Available from: http://www.ijri.org/article.asp?issn=0971-3026;year=2020;volume=30;issue=2;spage=240;epage=243;aulast=Desai;type=0