Indian Journal of Radiology and Imaging Indian Journal of Radiology and Imaging

NEURORADIOLOGY & HEAD AND NECK IMAGING
Year
: 2018  |  Volume : 28  |  Issue : 2  |  Page : 161--164

First case of neurofibromatosis with posterior reversible encephalopathy syndrome showing spinal cord involvement


Pui Kwan Joyce Chan, Kin Sun Tse, Wing Shan Elaine Fok, Wai Lun Poon 
 Department of Radiology and Imaging, Queen Elizabeth Hospital, Kowloon, Hong Kong (SAR), People's Republic of China

Correspondence Address:
Dr. Pui Kwan Joyce Chan
Department of Radiology & Imaging, 1/F, Block H, Queen Elizabeth Hospital, 30 Gascoigne Road, Kowloon, Hong Kong (SAR)
People's Republic of China

Posterior reversible encephalopathy syndrome (PRES) is a well-documented pathology of the brain in systemic upsets. Majority of PRES cases present with edema in the cerebrum, most commonly in the territory of posterior circulation. It has been reported to show spinal cord involvement in a rare subgroup known as PRES with spinal cord involvement (PRES-SCI), with very limited existing literature even in adult patients. Our institution recently encountered a pediatric case with neurofibromatosis type I (NF 1) showing PRES with extensive reversible spinal cord changes. This case illustrates the features of this rare entity in the pediatric group of patients, and is the first reported case in NF 1 patients.


How to cite this article:
Chan PK, Tse KS, Fok WS, Poon WL. First case of neurofibromatosis with posterior reversible encephalopathy syndrome showing spinal cord involvement.Indian J Radiol Imaging 2018;28:161-164


How to cite this URL:
Chan PK, Tse KS, Fok WS, Poon WL. First case of neurofibromatosis with posterior reversible encephalopathy syndrome showing spinal cord involvement. Indian J Radiol Imaging [serial online] 2018 [cited 2020 Aug 10 ];28:161-164
Available from: http://www.ijri.org/article.asp?issn=0971-3026;year=2018;volume=28;issue=2;spage=161;epage=164;aulast=Chan;type=0