Indian Journal of Radiology and Imaging Indian Journal of Radiology and Imaging

NEURORADIOLOGY & HEAD AND NECK IMAGING
Year
: 2018  |  Volume : 28  |  Issue : 1  |  Page : 18--21

Clinicoradiological aspects of pontine tegmental cap dysplasia: Case report of a rare hindbrain malformation


Aanchal Bhayana1, Sunil K Bajaj1, Ritu N Misra1, S Senthil Kumaran2 
1 Department of Radiodiagnosis, Safdarjung Hospital and VM Medical College, New Delhi, India
2 Department of Nuclear Medical Resonance, All India Institute of Medical Sciences, New Delhi, India

Correspondence Address:
Dr. Aanchal Bhayana
Department of Radiodiagnosis, Safdarjung Hospital and VM Medical College, New Delhi - 110 029
India

Malformations involving the brainstem are very rare and present with a varied spectrum of clinical symptoms due to multiple cranial nerve palsies and pyramidal tract involvement. Of these, pontine tegmental cap dysplasia is a very unusual malformation, characterized by ventral pons hypoplasia and an ectopic dorsal band of tissue, projecting into the fourth ventricle, from dorsal pontine tegmentum. A 4-year-old male child, presenting with left facial nerve palsy, revealed hypoplastic ventral pons and an ectopic structure on magnetic resonance imaging (MRI). The ectopic structure was isointense to pons, arose from the left side of dorsal pontine tegmentum, at pontomedullary junction and protruded into the fourth ventricle, impinging upon the left seventh and eighth cranial nerves. Diffusion tensor imaging (DTI) depicted abnormal white matter tracts in ectopic tissue with absent transverse pontine fibres and abnormal middle and superior cerebellar peduncles. The typical MRI appearance, coupled with DTI, helped us reach an accurate diagnosis of pontine tegmental cap dysplasia, in a setting of neurological dysfunction.


How to cite this article:
Bhayana A, Bajaj SK, Misra RN, Kumaran S S. Clinicoradiological aspects of pontine tegmental cap dysplasia: Case report of a rare hindbrain malformation.Indian J Radiol Imaging 2018;28:18-21


How to cite this URL:
Bhayana A, Bajaj SK, Misra RN, Kumaran S S. Clinicoradiological aspects of pontine tegmental cap dysplasia: Case report of a rare hindbrain malformation. Indian J Radiol Imaging [serial online] 2018 [cited 2020 Apr 6 ];28:18-21
Available from: http://www.ijri.org/article.asp?issn=0971-3026;year=2018;volume=28;issue=1;spage=18;epage=21;aulast=Bhayana;type=0