Indian Journal of Radiology and Imaging Indian Journal of Radiology and Imaging

NEURORADIOLOGY
Year
: 2010  |  Volume : 20  |  Issue : 4  |  Page : 245--249

MRI findings in Hirayama disease


Monali Raval1, Rima Kumari1, Aldrin Anthony Dung Dung2, Bhuvnesh Guglani3, Nitij Gupta3, Rohit Gupta4 
1 Department of Neuroradiology, Institute of Human Behaviour and Allied Sciences (IHBAS), Delhi, India
2 Department of Neurology, Institute of Human Behaviour and Allied Sciences (IHBAS), Delhi, India
3 Department of Neuroradiology, Focus Imaging and Research Institute, IHBAS Campus, Delhi, India
4 Department of Neuroradiology, B.K. Medical Centre, Delhi, India

Correspondence Address:
Rima Kumari
Associate Professor, Department of Neuroradiology, Institute of Human Behaviour and Allied Sciences (IHBAS), New Delhi
India

The objective of the study was to study the magnetic resonance imaging (MRI) features of Hirayama disease on a 3 Tesla MRI scanner. Nine patients with clinically suspected Hirayama disease were evaluated with neutral position, flexion, contrast-enhanced MRI and fast imaging employing steady-state acquisition (FIESTA) sequences. The spectrum of MRI features was evaluated and correlated with the clinical and electromyography findings. MRI findings of localized lower cervical cord atrophy (C5-C7), abnormal curvature, asymmetric cord flattening, loss of attachment of the dorsal dural sac and subjacent laminae in the neutral position, anterior displacement of the dorsal dura on flexion and a prominent epidural space were revealed in all patients on conventional MRI as well as with the dynamic 3D-FIESTA sequence. Intramedullary hyperintensity was seen in four patients on conventional MRI and on the 3D-FIESTA sequence. Flow voids were seen in four patients on conventional MRI sequences and in all patients with the 3D-FIESTA sequence. Contrast enhancement of the epidural component was noted in all the five patients with thoracic extensions. The time taken for conventional and contrast-enhanced MRI was about 30-40 min, while that for the 3D-FIESTA sequence was 6 min. Neutral and flexion position MRI and the 3D-FIESTA sequence compliment each other in displaying the spectrum of findings in Hirayama disease. A flexion study should form an essential part of the screening protocol in patients with suspected Hirayama disease. Newer sequences such as the 3D-FIESTA may help in reducing imaging time and obviating the need for contrast.


How to cite this article:
Raval M, Kumari R, Dung Dung AA, Guglani B, Gupta N, Gupta R. MRI findings in Hirayama disease.Indian J Radiol Imaging 2010;20:245-249


How to cite this URL:
Raval M, Kumari R, Dung Dung AA, Guglani B, Gupta N, Gupta R. MRI findings in Hirayama disease. Indian J Radiol Imaging [serial online] 2010 [cited 2020 Feb 16 ];20:245-249
Available from: http://www.ijri.org/article.asp?issn=0971-3026;year=2010;volume=20;issue=4;spage=245;epage=249;aulast=Raval;type=0