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Year : 1999  |  Volume : 9  |  Issue : 1  |  Page : 21-22
Images : Vein of galen malformation


Department of Radiology, MP Shah Cancer Hospital, Ahmedabad-380015, Gujrat, India

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Keywords: Vein of Galen Malformation, US, CT

How to cite this article:
Surana UM, Patel B N, Patel S B, Dhebar M. Images : Vein of galen malformation. Indian J Radiol Imaging 1999;9:21-2

How to cite this URL:
Surana UM, Patel B N, Patel S B, Dhebar M. Images : Vein of galen malformation. Indian J Radiol Imaging [serial online] 1999 [cited 2019 Nov 18];9:21-2. Available from: http://www.ijri.org/text.asp?1999/9/1/21/28366
An eight-months-old boy presented with features of macrocephaly and convulsions. Transcranial US [Figure - 1] revealed a sonolucent posterior third ventricular mass with internal echogenic turbulence with gross dilatation of both lateral and third ventricle. On CT [Figure - 2] there was evidence of an iso- to hyperdense midline mass posterior to the third ventricle with dilatation of both lateral and third ventricles, showing marked homogeneous enhancement. There was evidence of drainage into the straight sinus.

The term "vein of Galen malformation" is used to describe a heterogeneous group of anomalies with enlarged deep venous structures of the Galenic system, that are fed by abnormal midline arterio-venous communications [1] . Aneurysmal dilatation of the vein of Galen is the pathologic finding most common to this heterogeneous group of vascular malformations [2].

There are two basic types of vein of Galen malformation. In the first, single or multiple arteries drain directly into enlarged venous structures of the Galenic system. The most common anomaly is the singular multiple direct arterio-venous fistula between the choroidal and the quadrigeminal arteries and a median venous sac [3]. The sac probably represents persistence of a primitive venous channel that is the embryonic precursor of the vein of Galen. Some types of venous outflow restriction typically coexist with this type of vein of Galen malformation.

In the second type, a parenchymal AVM is present usually in the thalamus or midbrain and its nidus has deep Galenic drainage. Venous outflow constraints are also common in this group.

Diagnosis is made by transcranial US [Figure - 1], CT [Figure - 2], cerebral angiography, MR and MR angiography that can depict the arterial feeders and venous drainage pattern and delineate venous outflow restrictions.

 
   References Top

1.Osborn AG. Intracranial vascular malformations. In: Osborn AG, ed. Diagnostic Neuroradiology; 1 stsub edn, St. Louis: Mosby, 1998: 320-324.   Back to cited text no. 1    
2.Westra SJ, Guran JG. Pediatric intracranial vascular malformation. Radiology 1993; 186: 775-783.   Back to cited text no. 2    
3.Diebler C et al. Aneurysms of the vein of Galen in infants aged 2-15 months: diagnosis and natural evolution. Neuroradiology 1981; 21: 185-197.  Back to cited text no. 3    

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Correspondence Address:
Uday M Surana
1, Karnavati Bungalows, Near Shakti Petrol Pump, Sarkhej Gandhinagar Highway Satellite, Ahmedabad 380 015, Gujrat
India
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Source of Support: None, Conflict of Interest: None


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[Figure - 1], [Figure - 2]

This article has been cited by
1 Vein of Galen malformations: Review
Gupta, A.K., Varma, D.R.
Neurology India. 2004; 52(1): 43-53
[Pubmed]



 

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